Correct!
5. None of the above
Both Hughes-Stovin and Behçet syndrome are associated with pulmonary artery aneurysms (the former representing the combination of pulmonary artery or bronchial artery aneurysms and thrombophlebitis, and the latter representing a vasculitis presenting with oral and genital ulcers, arthritis, dermatologic manifestations, and posterior uveitis, in addition to pulmonary artery aneurysms); neither of these disorders is associated with pulmonary arteriovenous malformations. The hypogenetic lung syndrome is known by a number of other designations, including pulmonary venolobar syndrome and the “scimitar” syndrome. This disorder consists of the combination a hypoplastic thorax (typically the right thorax), often with dextroposition of the heart towards the most commonly affected right thorax, anomalous pulmonary venous drainage, and a hypoplastic (again usually) right pulmonary artery; pulmonary arteriovenous malformations are not a feature of this condition. While the lesion detected at chest radiography does indeed represent an arteriovenous malformation, the diagnosis of a sporadic, or isolated, arteriovenous malformation is not correct as illustrated in Figure 4.
Figure 4. Axial enhanced thoracic CT performed using a CT pulmonary angiography protocol shows that the medial right middle lobe lesion is an avidly enhancing pulmonary nodule (arrowhead). The tubular opacity seen in association with the nodule at chest radiography (Figures 1 and 2) is seen to reflect a large, enhancing pulmonary vessel (arrows). A second smaller nodule and third even smaller nodule (double arrowheads) are present in the subpleural region of the right lower lobe and left anterior base, respectively; these nodules are as also associated with enlarged vessels.
Which of the following is NOT associated with this patient’s diagnosis? (Click on the correct answer to be directed to the ninth of ten pages)